INFLAMMATORY DISEASES OF THE CENTRAL NERVOUS SYSTEM (320-326)

Bacterial meningitis
Meningitis due to other organisms
Meningitis of unspecified cause
Encephalitis, myelitis, and encephalomyelitis
Intracranial and intraspinal abscess
Phlebitis and thrombophlebitis of intracranial venous sinuses
Late effects of intracranial abscess or pyogenic infection

320 Bacterial meningitis


Includes: arachnoiditis bacterial
leptomeningitis bacterial
meningitis bacterial
meningoencephalitis bacterial
meningomyelitis bacterial
pachymeningitis bacterial

320.0 Hemophilus meningitis

Meningitis due to Hemophilus influenzae [H. influenzae]

320.1 Pneumococcal meningitis

320.2 Streptococcal meningitis

320.3 Staphylococcal meningitis

320.7 Meningitis in other bacterial diseases classified elsewhere

Code first underlying disease as:
actinomycosis (039.8)
listeriosis (027.0)
typhoid fever (002.0)
whooping cough (033.0-033.9)
Excludes: meningitis (in):
epidemic (036.0)
gonococcal (098.82)
meningococcal (036.0)
salmonellosis (003.21)
syphilis:
NOS (094.2)
congenital (090.42)
meningovascular (094.2)
secondary (091.81)
tuberculosis (013.0)

320.8 Meningitis due to other specified bacteria

320.81 Anaerobic meningitis
Gram-negative anaerobes
Bacteroides (fragilis)
320.82 Meningitis due to gram-negative bacteria, not elsewhere classified
Aerobacter aerogenes
Escherichia coli [E. coli] Friedlander bacillus
Klebsiella pneumoniae
Proteus morganii
Pseudomonas
Excludes: gram-negative anaerobes (320.81)
320.89 Meningitis due to other specified bacteria
Bacillus pyocyaneus

320.9 Meningitis due to unspecified bacterium

Meningitis:
bacterial NOS
purulent NOS
pyogenic NOS
suppurative NOS

321 Meningitis due to other organisms


Includes: arachnoiditis due to organisms other than bacteria
leptomeningitis due to organisms other than bacteria
meningitis due to organisms other than bacteria
pachymeningitis due to organisms other than bacteria

321.0 Cryptococcal meningitis

Code first underlying disease (117.5)

321.1 Meningitis in other fungal diseases

Code first underlying disease (110.0-118)
Excludes: meningitis in:
candidiasis (112.83)
coccidioidomycosis (114.2)
histoplasmosis (115.01, 115.11, 115.91)

321.2 Meningitis due to viruses not elsewhere classified

Code first underlying disease, as:
meningitis due to arbovirus (060.0-066.9)
Excludes: meningitis (due to):
abacterial (047.0-047.9)
adenovirus (049.1)
aseptic NOS (047.9)
Coxsackie (virus) (047.0)
ECHO virus (047.1)
enterovirus (047.0-047.9)
herpes simplex virus (054.72)
herpes zoster virus (053.0)
lymphocytic choriomeningitis virus (049.0)
mumps (072.1)
viral NOS (047.9)
meningo-eruptive syndrome (047.1)

321.3 Meningitis due to trypanosomiasis

Code first underlying disease (086.0-086.9)

321.4 Meningitis in sarcoidosis

Code first underlying disease (135)

321.8 Meningitis due to other nonbacterial organisms classified elsewhere

Code first underlying disease
Excludes: leptospiral meningitis (100.81)

322 Meningitis of unspecified cause


Includes: arachnoiditis with no organism specified as cause
leptomeningitis with no organism specified as cause
meningitis with no organism specified as cause
pachymeningitis with no organism specified as cause

322.0 Nonpyogenic meningitis

Meningitis with clear cerebrospinal fluid

322.1 Eosinophilic meningitis

322.2 Chronic meningitis

322.9 Meningitis, unspecified


323 Encephalitis, myelitis, and encephalomyelitis


Includes: acute disseminated encephalomyelitis
meningoencephalitis, except bacterial
meningomyelitis, except bacterial
myelitis (acute):
ascending
transverse
Excludes: bacterial:
meningoencephalitis (320.0-320.9)
meningomyelitis (320.0-320.9)

323.0 Encephalitis in viral diseases classified elsewhere

Code first underlying disease, as:
cat-scratch disease (078.3)
infectious mononucleosis (075)
ornithosis (073.7)
Excludes: encephalitis (in):
arthropod-borne viral (062.0-064)
herpes simplex (054.3)
mumps (072.2)
poliomyelitis (045.0-045.9)
rubella (056.01)
slow virus infections of central nervous system (046.0-046.9)
other viral diseases of central nervous system (049.8-049.9)
viral NOS (049.9)

323.1 Encephalitis in rickettsial diseases classified elsewhere

Code first underlying disease (080-083.9)

323.2 Encephalitis in protozoal diseases classified elsewhere

Code first underlying disease, as:
malaria (084.0-084.9)
trypanosomiasis (086.0-086.9)

323.4 Other encephalitis due to infection classified elsewhere

Code first underlying disease
Excludes: encephalitis (in):
meningococcal (036.1)
syphilis:
NOS (094.81)
congenital (090.41)
toxoplasmosis (130.0)
tuberculosis (013.6)
meningoencephalitis due to free-living ameba [Naegleria] (136.2)

323.5 Encephalitis following immunization procedures

Encephalitis postimmunization or postvaccinal
Encephalomyelitis postimmunization or postvaccinal
Use additional E code to identify vaccine

323.6 Postinfectious encephalitis

Code first underlying disease
Excludes: encephalitis:
postchickenpox (052.0)
postmeasles (055.0)

323.7 Toxic encephalitis

Code first underlying cause, as:
carbon tetrachloride (982.1)
hydroxyquinoline derivatives (961.3)
lead (984.0-984.9)
mercury (985.0)
thallium (985.8)

323.8 Other causes of encephalitis

323.9 Unspecified cause of encephalitis


324 Intracranial and intraspinal abscess


324.0 Intracranial abscess

Abscess (embolic):
cerebellar
cerebral
Abscess (embolic) of brain [any part]:
epidural
extradural
otogenic
subdural
Excludes: tuberculous (013.3)

324.1 Intraspinal abscess

Abscess (embolic) of spinal cord [any part]:
epidural
extradural
subdural
Excludes: tuberculous (013.5)

324.9 Of unspecified site

Extradural or subdural abscess NOS

325 Phlebitis and thrombophlebitis of intracranial venous sinuses


Embolism of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus
Endophlebitis of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus
Phlebitis, septic or suppurative of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus
Thrombophlebitis of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus
Thrombosis of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus
Excludes: that specified as:
complicating pregnancy, childbirth, or the puerperium (671.5)
of nonpyogenic origin (437.6)

326 Late effects of intracranial abscess or pyogenic infection


Note: This category is to be used to indicate conditions whose primary classification is to 320-325 [excluding 320.7, 321.0-321.8, 323.0-323.4, 323.6-323.7] as the cause of late effects, themselves classifiable elsewhere. The "late effects" include conditions specified as such, or as sequelae, which may occur at any time after the resolution of the causal condition.
Use additional code to identify condition, as:
hydrocephalus (331.4)
paralysis (342.0-342.9, 344.0-344.9)